The Disappearance of a Hepatic Mass in Anti-Synthetase Syndrome

Christopher J Mesa, MD*; Mona Arasoghli, MD; Pawan Suri, MD; Swati Pathak, MD; Shante Hinson, MD

 Lincoln Medical and Mental Health Center; Bronx, NY, USA

*Corresponding author: Christopher J Mesa, MD. Division of Rheumatology, Department of Internal Medicine, Lincoln Medical and Mental Health Center; Bronx, NY, USA. E-mail:Cmesa007@gmail.com

Published: June 16, 2017.  doi: 10.21103/Article7(2)_CR2

Abstract: 

Anti-Synthetase Syndrome (ASyS) is a rare chronic autoimmune disorder characterized by myositis, interstitial lung disease (ILD), polyarthralgia,  “mechanic’s hands” and Raynaud’s phenomenon. Liver lesions are quite rare in ASyS.  In our ASyS case, we will discuss a 58-year-old man presenting with muscle weakness, arthralgia, and interstitial lung disease (ILD). He was positive for anti-Jo-1 antibodies, substantiating the diagnosis, and was started on treatment. This was followed by the appearance of a liver mass that disappeared when the patient achieved remission.

Keywords: 
Anti-Synthetase Syndrome ● anti-Jo-1 antibody ● nodular regenerative hyperplasia ● treatment
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International Journal of Biomedicine. 2017;7(2):141-143. ©2017 International Medical Research and Development Corporation. All rights reserved.