Frantz Tumor, a Rare Indolent Pancreatic Neoplasm Entity: A Case Report and Brief Review

Faton T. Hoxha, Rrustem Musa, Shemsedin Hashani, Reshat Mati, Arb F. Hoxha, Nart F. Hoxha, Hasime Terziqi, Antigona Ukëhaxhaj

For citation: Hoxha FT, Musa R, Hashani S, Mati R, Hoxha AF, Hoxha NF, Terziqi H, Ukëhaxhaj A. Frantz Tumor, a Rare Indolent Pancreatic Neoplasm Entity: A Case Report and Brief Review. International Journal of Biomedicine. 2024;14(1):175-178. doi:10.21103/Article14(1)_CR5
Originally published March 1, 2024


Solid pseudopapillary neoplasm (SPN) of the pancreas, also known as Frantz tumor, is an uncommon tumor with indolent clinical features that primarily affects young women. We are presenting a 27-year-old Caucasian female with an accidental finding with pancreatic SPN who underwent complete resection of the tumor using a distal pancreatectomy and splenectomy procedure. Immunohistochemistry revealed low-grade pancreatic SPN. Despite the rare appearance, it should be considered in the differential diagnosis of a young female with a large pancreatic mass.

Frantz tumor • solid pseudopapillary neoplasm • pancreas • distal pancreatectomy
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Received December 12, 2023.
Accepted January 20, 2024.
©2024 International Medical Research and Development Corporation.